Sight:- In The Orbit Of The Eye
Age:- Average Age Of The Patients 7-8 Years Also Occurs In Adults.
Incidence:- It Is The Most Common Primary Malignancy Of The Orbit.
Diagnosis Of Orbital Rhabdomyosarcoma:-
Computed axial tomography (CT-scan) and magnetic resonance imaging (MRI) is usually used to see if the orbital bones have been attacked by the Rhabdomyosarcoma.
Symptoms Of Orbital Rhabdomyosarcoma:-
1. Droopy eyelid (called ptosis), and/or prominent eyes (called proptosis), or tumor under the conjunctiva.
Treatment Of Orbital Rhabdomyosarcoma:-
The main objective of surgery is to attain tissue through an excisional or incisional biopsy so that the pathological diagnosis can be done. Once the diagnosis is confirmed, the patient is referred to pediatric oncologists for proper management with chemotherapy and radiation.
The poor diagnosis for patients with orbital rhabdomyosarcoma and orbital exenteration encouraged the use of orbital irradiation. Patients in Groups II, III, and IV are suggested radiation in the range of 4000 to 5000 cGy during the course of 4 to 5 weeks. If there is an indication of intracranial spread, chemotherapy may be indicated.
Patients with a localized tumor are usually treated with chemotherapy alone. Groups II, III and IV receive a combination chemotherapy and radiation therapy. The stage of the cancer determines the duration and number of chemo for treatment. Vincristine and actinomycin are the conventional agents, but now newer agents, such as ifosfamide and etoposide, are also used. It is significant that the patient’s treatment schedule is handled by an experienced oncologist.